Search results for Branched-Chain Alpha-Ketoacid Dehydrogenase Kinase (BCKDK) Antibody
Branched-Chain Alpha-Ketoacid Dehydrogenase Kinase (BCKDK) Antibody, Abbexa, abx320636
BCKDK Antibody is a Rabbit Polyclonal against BCKDK.
Host
Rabbit
Reactivity
Human
Applications
ELISA, IHC
Conjugation
Unconjugated
Branched-Chain Alpha-Ketoacid Dehydrogenase Kinase (BCKDK) Antibody, Abbexa, abx033187
The second major step in the catabolism of the branched-chain amino acids, isoleucine, leucine, and valine, is irreversibly catalyzed by the branched-chain alpha-keto acid dehydrogenase complex (BCKD), an inner-mitochondrial enzyme complex composed of 3 catalytic components: a branched-chain alpha-keto acid decarboxylase (E1), a dihydrolipoyl transacylase (E2), and a dihydrolipoamide dehydrogenase (E3). The complex also contains 2 enzymes that regulated the state of activity of the BCKD complex: a kinase (BCKDK), and a phosphorylase. The ubiquitiously expressed kinase contains 1 histidine kinase domain. Maple syrup urine disease (MSUD) is a pathology secondary to an enzyme defect in the catabolic pathway of leucine, isoleucine, and valine. Accumulation of these amino acids and their corresponding keto acids results in encephalopathy and progressive neurodegeneration in infants not treated for MSUD.
Host
Rabbit
Reactivity
Human
Applications
ELISA, WB, IHC
Conjugation
Unconjugated
Branched-Chain Alpha-Ketoacid Dehydrogenase Kinase (BCKDK) Antibody, Abbexa, abx321495
BCKDK Antibody is a Rabbit Polyclonal against BCKDK.
Host
Rabbit
Reactivity
Human
Applications
ELISA, WB, IHC
Conjugation
Unconjugated
Branched-Chain Alpha-Ketoacid Dehydrogenase Kinase (BCKDK) Antibody, Abbexa, abx171470
This product is currently in development. The lead time for this product may be several months. Please contact us at [email protected] for an updated lead time before purchasing this product. Branched-Chain Alpha-Ketoacid Dehydrogenase Kinase (BCKDK) Antibody is a Mouse Monoclonal antibody against Branched-Chain Alpha-Ketoacid Dehydrogenase Kinase (BCKDK).
Host
Mouse
Reactivity
Rat
Applications
WB, IHC, IF/ICC
Conjugation
Unconjugated
Branched-Chain Alpha-Ketoacid Dehydrogenase Kinase (BCKDK) Antibody, Abbexa, abx130391
Branched-Chain Alpha-Ketoacid Dehydrogenase Kinase Antibody is a Rabbit Polyclonal against Branched-Chain Alpha-Ketoacid Dehydrogenase Kinase.
Host
Rabbit
Reactivity
Rat
Applications
WB, IHC, IF/ICC
Conjugation
Unconjugated
Branched-Chain Alpha-Ketoacid Dehydrogenase Kinase (BCKDK) Antibody, Abbexa, abx027612
Catalyzes the phosphorylation and inactivation of the branched-chain alpha-ketoacid dehydrogenase complex, the key regulatory enzyme of the valine, leucine and isoleucine catabolic pathways. Key enzyme that regulate the activity state of the BCKD complex (By similarity).
Host
Rabbit
Reactivity
Human, Mouse
Applications
ELISA, WB
Conjugation
Unconjugated
Branched-Chain Alpha-Ketoacid Dehydrogenase Kinase (BCKDK) Antibody, Abbexa, abx006092
BCKDK Antibody is a Rabbit Polyclonal Antibody against BCKDK.
Host
Rabbit
Reactivity
Human, Rat
Applications
ELISA, WB, IF/ICC
Conjugation
Unconjugated
Branched-Chain Alpha-Ketoacid Dehydrogenase Kinase (BCKDK) Antibody, Abbexa, abx033169
The second major step in the catabolism of the branched-chain amino acids, isoleucine, leucine, and valine, is irreversibly catalyzed by the branched-chain alpha-keto acid dehydrogenase complex (BCKD), an inner-mitochondrial enzyme complex composed of 3 catalytic components: a branched-chain alpha-keto acid decarboxylase (E1), a dihydrolipoyl transacylase (E2), and a dihydrolipoamide dehydrogenase (E3). The complex also contains 2 enzymes that regulated the state of activity of the BCKD complex: a kinase (BCKDK), and a phosphorylase. The ubiquitiously expressed kinase contains 1 histidine kinase domain. Maple syrup urine disease (MSUD) is a pathology secondary to an enzyme defect in the catabolic pathway of leucine, isoleucine, and valine. Accumulation of these amino acids and their corresponding keto acids results in encephalopathy and progressive neurodegeneration in infants not treated for MSUD.
Host
Rabbit
Reactivity
Human, Mouse
Applications
ELISA, WB
Conjugation
Unconjugated
Branched-Chain Alpha-Ketoacid Dehydrogenase Kinase (BCKDK) Antibody, Abbexa, abx329448
BCKDK Antibody is a Rabbit Polyclonal against BCKDK.
Host
Rabbit
Reactivity
Human, Mouse, Rat
Applications
ELISA, WB, IHC, IF/ICC
Conjugation
Unconjugated
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